A Clinical Case of Pulmonary Lymphangioleiomyomatosis
https://doi.org/10.21292/2075-1230-2022-100-2-44-47
Abstract
The article describes a clinical case of pulmonary lymphangioleiomyomatosis (LAM) in a 44-year-old female Patient N., who has been suffering from this disease for a long time. It depicts characteristic classic signs of LAM – a progressive course, thin-walled air cavities in the lungs, retroperitoneal lymphadenopathy, and recurrent pneumothoraxes.
About the Authors
S. S. Kazakova
Ryazan State Medical University Named after I.P. Pavlov
Russian Federation
Russian Federation
Svetlana S. Kazakova - Associate Professor at Phthisiology Department with Training in X-ray Diagnostics.
9, Vysokovoltnaya St., Ryazan, 390026. Phone: 8 (4912) 97-18-01
E. V. Аftaeva
Ryazan State Medical University Named after I.P. Pavlov
Russian Federation
Russian Federation
Elena V. Аftaeva - Assistant of Phthisiology Department with Training in X-ray Diagnostics.
9, Vysokovoltnaya St., Ryazan, 390026. Phone: 8 (4912) 97-18-01
Z. V. Zinovieva
Ryazan State Medical University Named after I.P. Pavlov
Russian Federation
Russian Federation
Zoya V. Zinovieva - Resident Physician at Phthisiology Department with Training in X-ray Diagnostics.
9, Vysokovoltnaya St., Ryazan, 390026. Phone: 8 (4912) 97-18-01
References
1. Kazakova S.S., Khazov P.D., Kolesov V.Yu. MSCT in the diagnosis of lymphocytic pneumonia. Mat-ly Mezhregion. Nauch. Konf. RyazGMU Im. Akad. I.P. Pavlova. [Abst. Book of Inter-Regional Research Conference of Ryazan State Medical University Named after I.P. Pavlov]. 2014, pp. 121-124. (In Russ.)
2. Shashina M.M., Shapovalova T.G., Kazimirova N.E., Ryabova А.Yu., Аrkhangelskaya E.E., Lifanova D.V., Chernyshkova M.А. Pulmonary lymphangioleiomyomatosis (a clinical case). Saratovsky Nauchno-Meditsinsky Journal, 2017, vol. 13, no. 4, pp. 828-833. (In Russ.)
3. Ataya A., Brantly M., Riley L. Lymphangioleiomyomatosis (LAM). Am. J. Respir. Crit. Care Med., 2018, vol. 198, no. 4, pp. P7-P8.
4. Bissler J.J., Kingswood J.C., Radzikowska E. et al. Everolimus long-term use in patients with tuberous sclerosis complex: Four-year update of the EXIST-2 study. PLoS One, 2017, vol. 12, no. 8, pp. e0180939.
5. Johnson S.R., Cordier J.F., Lazor R. et-al. European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis. Eur. Respir. J., 2010, vol. 35, no. 1, pp. 14-26. doi:10.1183/09031936.00076209, Pubmed citation.
6. Liu J., Zhao W., Ou X. et al. Mutation spectrums of TSC1 and TSC2 in Chinese women with lymphangioleiomyomatosis (LAM). PLoS One, 2019, vol. 14, no. 12, pp. e0226400.
7. Oberstein E.M., Fleming L.E., Gomez-Marin O., Glassberg M.K. Pulmonary lymphangioleiomyomatosis (LAM): examining oral contraceptive pills and the onset of disease. J. Womens Health (Larchmt), 2003, vol. 12, no. 1, pp. 81-85.
8. Sclafani A., VanderLaan P. Lymphangioleiomyomatosis. N. Engl. J. Med., 2018, vol. 378, no. 23, pp. 2224.
9. Silva D.L., Pinto P., Costa M., Maia R., Rodrigues C. Pneumothorax as a presentation of tuberous sclerosis-associated lymphangioleiomyomatosis. Eur. J. Case Rep. Intern. Med., 2019, vol. 6, no. 10, pp. 001264.
10. Travis W.D., Brambilla E., Nicholson A.G. et al, for the WHO Panel. The 2015 World Health Organization Classification of Lung Tumors: impact of genetic, clinical and radiologic advances since the 2004 classification. J. Thorac. Oncol., 2015, vol. 10, no. 9, pp. 1243-1260.
Review
For citations:
Kazakova S.S., Аftaeva E.V., Zinovieva Z.V. A Clinical Case of Pulmonary Lymphangioleiomyomatosis. Tuberculosis and Lung Diseases. 2022;100(2):44-47. (In Russ.) https://doi.org/10.21292/2075-1230-2022-100-2-44-47
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